Slide Anak - Marasmus Ok

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    Case Report: MarasmusMona Claudya110100341

    Yujinee Devi 110100468

    Supervisor:dr. Hj. Tiangsa Se!iring" M.#ed $%ed&" Sp.'$#&

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    Protein

    EnergyMalnutrition

    4() o* +,e10.4 illion

    dea+,s in-,ildren

    /years

    0) o* +,eorld2s

    alnouris,ed-,ildren live

    in 'sia

    3 *ors:

    Marasus

    #as,ioror 

    Marasi-as,ioror 

    Suspe-+i!le+o in*e-+ion

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    Diagnos+i- *ea+ures:

    • 5eig,+*orleng+,,eig,+

    3SD $severe as+ed&• Midupper ar

    -ir-u*eren-e 11/

    • 7edea o* !o+, *ee+

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    S+a!ilia+ion %,ase

    Transi+ional %,ase

    9e,a!ili+a+ion %,ase

    olloup %,ase

    Treatment of PEM

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    .Objective

    T,e ai o* +,is s+udy is +o repor+ a -ase o* a ( on+,sold !oy i+, diagnosis o* arasus and gas+roin+es+inal

     !leeding

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    Case

    '#" ( on+,s old !oy as adi++ed on 7-+o!er" 1/+, ;01/ i+,

    -oplain+ o* losing appe+i+e and eig,+ loss.

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    •History of previous illness:He ,ad ever !een ,ospi+alied in Haji 'da MaliHospi+al on uly ;01/ ,en ,e as 6 on+,s old *or+,e !la- s+ool diarr,ea. '*+er !eing dis-,arged" ,e

    never go+ +o -on+rol and go+ any edi-a+ion +o do-+or*or ,is illness. He su**ered *ro re-urren+ !la- s+oolin pas+ 8 days.

    • History of immunization : no+ -lear 

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    •History of nutrition: 6 on+, o* e=-lusive !reas+ *eeding" addi+ional *ood sin-e 6on+,s old

    • History of obstetric: +,e o+,er as 38 years old ,en s,e as pregnan+" no,is+ory o* -onsuing drugs and ,er!s" no ,is+ory o* ,avingDM and ,yper+ension during pregnan-y

    • History of growth an evelopment: 

    '+ +,e oen+" +,e pa+ien+ -ould si+ don i+, assis+an-e

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     Presence status

    • Cons-iousness : aler+

    Elood %ressure : (040 Hg• Hear+ 9a+e : 1;4 =i

    • 9espira+ory 9a+e : 30 =i

    •Eody Tepera+ure : 3"( oC

    • 'nei- $@&

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     Local Status

      Headoldan *a-e" iso-,ori- pupil" pale in*erior palpe!ra

    -onjun-+iva" lig,+ re*le= on !o+, eyes. Bars nose ou+,:

    i+,in noral lii+

    •   Neck 

     Go lyp, node enlargeen+

    •   Thorax

    Sye+ri-al *usi*oris" in+er-os+al spa-e -learly visi!le" pro+ruding spine. H9: 1;0=i" regular" urur $&. 99:

    ;3=i" regular" ron-,i $&" !rea+, sound: vesi-ular"

    addi+ional sound $&

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    •  Abdomen

    Soepel" noral peris+al+i-" liver and spleen

    unpalpa!le" sin pin-, re+urns >ui-ly

    •  Extremities

    Hypo+,rop,y us-le" su!-u+aneous *a+

    +,inning. %ulse 1;0=i" regular" ade>ua+e pressure and volue" ar" C9T 3" no

     pi++ing edea

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    "ifferential "iagnosis:

    • Marasus @ Ias+roin+es+inal !leeding @

    Haeor,agi- aneia• Marasus @ Ias+roin+es+inal !leeding @ 'neia

    o* -,roni- disease

    #or$ing "iagnosis:

    • Marasus @ Ias+roin+es+inal !leeding @

    Haeor,agi- aneia

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    Management:

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    "iagnostic Planning:• Cople+e Elood Tes+

    • rine and *es-es analysis

    eru %ro*ile• rine and es-es B=aina+ion

    • %lain a!doinal =ray

    • Eariu eal• 'l!uin

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    %aboratory &ining: October '(th ) *+'(

    ro +,e +a!le a!ove" e *ound aneia and +,ro!o-y+openia.

    Haematology Result ,ormal

    Haeoglo!in gdF -.++ 11.1 J 14.4

    Bri+ro-y+e ;.43 3.1 4.;/

    Feu-o-y+e 1/.83 6.0 1./

    Haea+o-ri+e ) ;;.0 3/ 41

    T,ro!o-y+e '(/ ;1 J 4(

    MC? *F (0./0 8; 100

    MCH pg ;8.80 ;4 30

    MCHC g ) 31.80 ;8 3;

    9D5 ) ;1.40 14.( 18.

     Geu+ro*il ) 66.30 3 80

    Fip,o-y+e ) 1(.10 ;0 40

    Mono-y+e ) 11.;0 ; 8

    Bosino*il ) 3.30 1 6

    Easo*il ) 0.100 0 1

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    Haemostasis Result ,ormal

    %ro+,ro!in Tie

    • %a+ien+

    • Con+rol

    se-onds

    se-onds

    1.;

    13.8

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    0rinalysis Complete 0rine Result ,ormal

    Color Yello -lear Yello

    Ilu-ose Gega+ive Gega+ive

    Eiliru!in Gega+ive Gega+ive

    #e+on Gega+ive Gega+ive

    Spesi*i- gravi+y 1.000 1.00/ J 1.030

     pH .0 / 8

    %ro+ein Gega+ive Gega+ive

    ro!ilinogen Gega+ive Gi+ri+ Gega+ive Gega+ive

    Feu-o-y+e Gega+ive

    Elood Gega+ive Gega+ive

    rine Sedien+Bry+ro-y+e F%E 01 3

    Feu-o-y+e F%E 01 6

    Bpi+el F%E 01

    Cas+s F%E Gega+ive Gega+ive

    Cris+al F%E Gega+ive

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    &esces Result ,ormal

    Ma-ros-opi-

    Color Eron

    Consis+en-y 5a+ery

    Elood Gega+ive Gega+ive

    Mu-us Gega+ive Gega+ive

    Mi-ros-opi-

    Bgg or F%E Gega+ive Gega+ive

    'oe!a F%E Gega+ive Gega+ive

    Bry+ro-y+e F%E 01

    Feu-o-y+e 01

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    1arium Meal: October '2th) *+'(

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    Plain 3bominal 45ray : October '6th) *+'(

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    S Fos+ appe+i+e" !loody voi+ $@& and !loody s+ool $@&

    7

    Sens : 'ler+" T : 3"( C" E5 : 4"(g" EH : 64-

    Head: eye re*le-+ @@" iso-or" pale -onj. palpe!ra in*erior@@"

    BarGoseMou+,: noral

     Ge-: ?% 9@; - H;7

    T,ora= : Sye+ri-al *usi*or" re+ra-+ion $&" H9 : 1;/=

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    P  78&" "(9 ,aCl +)**(9 *+gtti ;micro<

     &olic aci '!' mg

    8itamin 1 Comple! '!' tab 8itamin C '!' tab

     "iet &-( /+ cc= hours > ')2 cc mineral mi!

    ?ransfusion PRC *( cc*@ jam

    7nj Ceftria!one *(+ mg'* hoursiv

    Consul+ gas+ro,epa+ology division

    Consul+ ,ea+oon-ology division

    Consul+ nu+ri+ion and e+a!oli- disease division

    Cople+e urine and *es-es analysis

    C,e- iron pro*ile

    %erip,eral !lood sear 

    Eariu Meal

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    S Fos+ appe+i+e" !loody voi+ $&" !loody s+ool $&" *ever $@&

    7

    Sens : 'ler+" T : 3" C" E5 : 4"(g" EH : 64-Head: eye re*le-+ @@" iso-or" pale -onj. %alpe!ra in*erior" BarGoseMou+,:

    noral

     Ge-: ?% 9@; - H;7

    T,ora= : Sye+ri-al *usi*or" re+ra-+ion $&" H9 : 100=

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    P  78&" "(9 ,aCl +)**(9 *+gtt7 ;micro<

     &olic aci '!'mg

    8itamin 1 Comple! '!' tab

    8itamin C '!(+mg

     "iet &-( /+cc= hours > ')2cc mineral mi!

    ?ransfusion PRC *(cc*@jam

    7nj ceftria!one *(+mg'*hoursiv

    S-,eduled *or '!doinal Kray

    B=pe-+ing Eariu Meal resul+

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    S Fos+ appe+i+e" !loody s+ool $&" *ever $&

    7 Sens : 'ler+" T : 3"/ C" E5 : 4"(g" EH : 64-

    Head: eye re*le-+ @@" iso-or" pale -onj. %alpe!ra in*erior"

    BarGoseMou+,: noral

     Ge-: ?% 9@; - H;7

    T,ora= : Sye+ris *usi*oris" re+ra-+ion $&" H9 : 100=

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    %

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    S Eloody s+ool $&" *ever $@&

    7 Sens : 'ler+" T : 3"6 C" E5 : 4"(g" EH : 64-

    Head: eye re*le-+ @@" iso-or" pale -onj. %alpe!ra in*erior @@"

    BarGoseMou+,: noral

     Ge-: ?% 9@; - H;7

    T,ora= : Sye+ri-al *usi*or" re+ra-+ion $&" H9 : (;=

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    7 9esul+ *ro Gu+ri+ion and e+a!oli- disease division:

    ood re-all ;4 ,ours:

    Morning: porridge1; por+ion @ -arro+ L pie-e'*+ernoon: porridge L por+ion @ po+a+o L pie-e

     Gig,+: porridge L por+ion @ -arro+ L pie-e

    Ereas+ *eeding on deand.

    T,erapy : die+ / 80--3 ,ours @ 1"6-- ineral i=

    ?i+. ' 100.000 uni+ $1=& ?i+.E -op 1=1 +a!

    ?i+.- 1=/0g

    Co+rio=aole ;= L +spn

     

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    ' Marasus

    Ias+roin+es+inal !leeding

    'neia

    %  

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    S Fos+ appe+i+e" !loody s+ool $&" *ever $&

    7 Sens : 'ler+" T : 3 C" E5 : /g" EH : 64-Head: eye re*le-+ @@" iso-or" pale -onj. %alpe!ra in*erior @@"

    BarGoseMou+,: noral

     Ge-: ?% 9@; - H;7

    T,ora= : Sye+ris *usi*oris" re+ra-+ion $&" H9 : (8=

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    %

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    Dis-ussion

    M'9'SMS

    De*i-ien-y calories and energy" o--urainly a+ +,e +ieo* eaning $/yo&

    ,utritional status$E5EH&

    5H7 ;006: /years

    CDC ;000: /years

    Clinical Manifestation

    7ld an *a-e" irri+a!le" us-le,ypo+rop,y" su!-u+aneous *a+loss" pianosign" !aggypan+s

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    Des-reasedin p,ysi-al

    a-+ivi+ylethargy

    De-reased !asal energye+a!olis

    Alowing ofgrowth

    #eight loss

     Gega+ive energy !alan-e

    De-reased energy in+ae

    Foss o* inges+ed -alories $eesis"

    diarr,ea" !urns&

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    • Eody *luid -opar+en+

    Hig, +o+al !ody a+er" signi*i-an+ redu-+ion in adipose and lean

    ass" us-le -ell a+rop,y ar -ir-u*eren-e

    • Me+a!oli- adap+a+ion

    siilar +o s+arva+ion" redu-ed energy e+a!olis ris o*

    ,ypo+,eria

    • Diges+ive +ra-+

    villous a+rop,y o* jejunal u-osa" de-reased HCl e=-re+ion"

    sloing peris+alsis !a-+erial overgro+,

    • Bndo-rine sys+e

    *ree plasa level o* -or+isol N in ,ypoal!uineia

    • Cardiovas-ular 

    saller and +,inner -ardia- us-le" loer s+roe volue"

     !radi-ardia and ,ypo+ension

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    Trea+en+ o* severe alnu+ri+ion

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    Case:

    Day 1 J day $+,e s+a!ilia+ion and +ransi+ion

     p,ase &

    80-- / every 3 ,ours and 1"6-- ineral

    i=

    Day 8 $s+ar+ re,a!ili+a+ion p,ase&

    -a+-,up *eeding 100 80-- every 3 ,ours and

    1"6-- ineral i=

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    Moni+oring

    • %oor $ / gg per day&" reassessen+

    • Modera+e $/J10 gg per day&" -,e- in+ae

    +arge+s are !eing e+ or in*e-+ion

    • Iood $ 10 gg per day&

    Case:Poor: +,e eig,+ gain 1gr on re,a!ili+a+ion p,ase

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    Suary

    '#" ( on+,s old !oy as adi++ed on 7-+o!er" 1/ +, ;01/ i+,-oplain+ o* losing appe+i+e" eig,+ loss" ,aving !la- s+ool.

    %a+ien+ as diagnosed i+, Marasus @ Ias+roin+es+inal

     !leeding @ 'neia pos+ ,eorr,agi-. %a+ien+ as given

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     Thank You